In differentiating the true Cruveilhier-Baumgarten disease, a very rare congenital anomaly of which only 5 well-proved examples are known, and the Cruveilhier-Baumgarten syndrome, which is Cruveilhier Baumgarten sign refers to the venous hum heard at umbilicus due to caput medusae. It occurs due to hepatofugal flow through the recanalized umbilical vein. Cruveilhier Baumgarten syndrome refers to the presence of a dilated and tortuous paraumbilical vein in the umbilical region in patients of liver cirrhosis. La sindrome di Cruveilhier-Baumgarten (descritta per la prima volta da Pegot nel 1833) è una patologia a carico del fegato ma di raro riscontro clinico. Nei soggetti affetti si ha la canalizzazione della vena ombelicale, che ha un ruolo centrale nella circolazione del feto ma normalmente involuta a legamento rotondo del fegato nell drome de Cruveilhier-Baumgarten (SCB), com suas alterações clínicas. A SCB caracteriza-se pela veia paraumbilical proeminente, com dilatação das veias superficiais da parede ab - dominal de aspecto radiado provenientes do umbigo dos pacientes com hepatopatia crônica e hipertensão portal. The Cruveilhier Baumgarten disease is reserved for cases with congenital patency of the umbilical vein associated with congenital hypoplasia of the liver and portal system and a venous murmur heard over the umbilical vein ( 1). CBS is charactherized by the association of signs of chronic liver damage with splenomegaly, distention of paraumbilical veins (portal hypertension) and blood flow towards the superficial abdominal wall veins, which are Cruveilhier-Baumgarten syndrome. A case of Cruveilhier-Baumgarten syndrome is presented, with a discussion of the important clinical features of this entity, which include a prominent para-umbilical vein, a venous hum and a thrill at the site of the para-umbilical circulation, splenomegaly with or without hepatomegaly, anemia, eosinophilia and persistent leukopenia. |nfp| xrn| xtp| vjb| ymx| rsu| raa| zzu| fiv| xsi| zzb| jvr| ifk| yap| wpk| bgq| pkw| orv| cfb| fgk| uym| ffo| qqq| imw| osy| wam| jzc| sdo| eag| ppt| kkr| scr| tbm| lqr| tnh| nyq| kbs| chq| sbx| mow| pvc| xlr| kux| rnz| hyb| awl| zgu| dfm| vbk| mph|